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Adult-onset Krabbe disease in two generations of a Chinese family 期刊论文
ANNALS OF TRANSLATIONAL MEDICINE, 2018, 卷号: 6, 期号: 10
作者:  Zhang, Tongxia;  Yan, Chuanzhu;  Ji, Kunqian;  Lin, Pengfei;  Chi, Lingyi
收藏  |  浏览/下载:15/0  |  提交时间:2019/12/11
ETFDH Mutations and Flavin Adenine Dinucleotide Homeostasis Disturbance Are Essential for Developing Riboflavin-Responsive Multiple Acyl-Coenzyme A Dehydrogenation Deficiency 期刊论文
ANNALS OF NEUROLOGY, 2018, 卷号: 84, 期号: 5, 页码: 659-673
作者:  Xu, Jingwen;  Li, Duoling;  Lv, Jingwei;  Xu, Xuebi;  Wen, Bing
收藏  |  浏览/下载:5/0  |  提交时间:2019/12/11
Role of the chemokine receptors CXCR3, CXCR4 and CCR7 in the intramuscular recruitment of plasmacytoid dendritic cells in dermatomyositis 期刊论文
JOURNAL OF NEUROIMMUNOLOGY, 2018, 卷号: 319, 页码: 142-148
作者:  Lv, Jingwei;  Li, Ling;  Li, Wei;  Ji, Kunqian;  Hou, Ying
收藏  |  浏览/下载:13/0  |  提交时间:2019/12/11
Growth Differentiation Factor 15 Is a Novel Diagnostic Biomarker of Mitochondrial Diseases 期刊论文
MOLECULAR NEUROBIOLOGY, 2017, 卷号: 54, 期号: 10, 页码: 8110-8116
作者:  Ji, Xinbo;  Zhao, Lizhen;  Ji, Kunqian;  Zhao, Yuying;  Li, Wei
收藏  |  浏览/下载:6/0  |  提交时间:2019/12/12
Identification of miRNA, lncRNA and mRNA-associated ceRNA networks and potential biomarker for MELAS with mitochondrial DNA A3243G mutation 期刊论文
SCIENTIFIC REPORTS, 2017, 卷号: 7
作者:  Wang, Wei;  Zhuang, Qianqian;  Ji, Kunqian;  Wen, Bing;  Lin, Pengfei
收藏  |  浏览/下载:4/0  |  提交时间:2019/12/12
Role of Toll-like receptors and retinoic acid inducible gene I in endogenous production of type I interferon in dermatomyositis 期刊论文
JOURNAL OF NEUROIMMUNOLOGY, 2015, 卷号: 285, 页码: 161-168
作者:  Li, Ling;  Dai, Tingjun;  Lv, Jingwei;  Ji, Kunqian;  Liu, Junling
收藏  |  浏览/下载:5/0  |  提交时间:2019/12/17
Idebenone protects against oxidized low density lipoprotein induced mitochondrial dysfunction in vascular endothelial cells via GSK3 beta/beta-catenin signalling pathways 期刊论文
Biochemical and Biophysical Research Communications, 2015, 卷号: 465, 期号: 3, 页码: 548-555
作者:  Lin, Pengfei;  Liu, Junling;  Ren, Ming;  Ji, Kunqian;  Li, Ling
收藏  |  浏览/下载:4/0  |  提交时间:2019/12/17
Skeletal muscle increases FGF21 expression in mitochondrial disorders to compensate for energy metabolic insufficiency by activating the mTOR-YY1-PGC1 alpha pathway 期刊论文
FREE RADICAL BIOLOGY AND MEDICINE, 2015, 卷号: 84, 页码: 161-170
作者:  Ji, Kunqian;  Zheng, Jinfan;  Lv, Jingwei;  Xu, Jingwen;  Ji, Xinbo
收藏  |  浏览/下载:4/0  |  提交时间:2019/12/17
Skeletal muscle increases FGF21 expression in mitochondrial disorders to compensate for energy metabolic insufficiency by activating the mTOR-YY1-PGC1 alpha pathway 期刊论文
Free Radical Biology and Medicine: The Official Journal of the Oxygen Society, 2015, 页码: 161-170
作者:  Ji, Kunqian;  Zheng, Jinfan;  Lv, Jingwei;  Xu, Jingwen;  Ji, Xinbo
收藏  |  浏览/下载:4/0  |  提交时间:2019/12/17
Mesenchymal stem cells rescue injured endothelial cells in an in vitro ischemia-reperfusion model via tunneling nanotube like structure-mediated mitochondrial transfer 期刊论文
MICROVASCULAR RESEARCH, 2014, 卷号: 92, 页码: 10-18
作者:  Liu, Kaiming;  Ji, Kunqian;  Guo, Liang;  Wu, Wei;  Lu, Huixia
收藏  |  浏览/下载:3/0  |  提交时间:2019/12/17


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